No clinical details are available regarding this patient.
The specimen is a small kidney, 9 cm in length, which has been bisected in its long axis and mounted to display the cut surface. Arising from the lateral border of the kidney there is an ovoid tumour, 16 x 8 cm in diameter. The tumour is attached to the kidney and has replaced most of the renal parenchyma in the mid-zone. The cut surface of the tumour shows a mass of thin-walled cysts, ranging from one millimetre to 2.5 cm in diameter. In the mid-zone at the periphery of the tumour, there is a more solid area, 2 x 1 cm in diameter. This is a lymphangioma of the kidney.
Lymphangioma of the kidney is a very rare tumour, usually occurring in infants or children. Typically, it is large, unencapsulated and replaces part of the kidney. Histologically, the cystic spaces are lined by a single layer of flattened endothelial cells. Malignant change does not occur.